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Compound heterozygous mutations in KCNJ2 and KCNH2 in a patient with severe Andersen-Tawil syndrome

Andersen-Tawil syndrome (ATS) is a rare channelopathy, sometimes referred to as long QT syndrome type 7. ATS is an autosomal dominant disease predominantly caused by mutations in the KCNJ2 gene. Patients with ATS present with episodes of muscle weakness, arrythmias, including prolonged QT intervals,...

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Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:BMJ Case Rep
Egile Nagusiak: Polyak, Margarita E, Shestak, Anna, Podolyak, Dmitriy, Zaklyazminskaya, Elena
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BMJ Publishing Group 2020
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC7449271/
https://ncbi.nlm.nih.gov/pubmed/32843460
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2020-235703
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