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Systemic AL Amyloidosis: Current Approaches to Diagnosis and Management

AL amyloidosis is characterized by a low-level expansion of an indolent, small plasma cell clone that produces amyloidogenic light chains. Amyloid aggregates or preceding intermediaries cause direct cell damage through their proteotoxicity, and amyloid deposits distort tissue architecture, and, even...

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Detalhes bibliográficos
Publicado no:Hemasphere
Main Authors: Fotiou, Despina, Dimopoulos, Meletios Athanasios, Kastritis, Efstathios
Formato: Artigo
Idioma:Inglês
Publicado em: Wolters Kluwer Health 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7430233/
https://ncbi.nlm.nih.gov/pubmed/32885146
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/HS9.0000000000000454
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