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Clinicopathological correlations of sural nerve biopsies in TTR Val30Met familial amyloid polyneuropathy

Familial amyloid polyneuropathy with the substitution of methionine for valine at position 30 in the TTR gene is the most common type of hereditary transthyretin amyloidosis. Although several authors have previously reported a size-dependent fibre loss, predominantly involving unmyelinated and small...

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Salvato in:
Dettagli Bibliografici
Pubblicato in:Brain Commun
Autori principali: Fernandes, Armindo, Coelho, Teresa, Rodrigues, Aurora, Felgueiras, Helena, Oliveira, Pedro, Guimarães, António, Melo-Pires, Manuel, Taipa, Ricardo
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7425381/
https://ncbi.nlm.nih.gov/pubmed/32954271
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/braincomms/fcz032
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