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Relationship between markers of disease activity and progression in skeletal muscle of GNE myopathy patients using quantitative nuclear magnetic resonance imaging and (31)P nuclear magnetic resonance spectroscopy

BACKGROUND: Quantitative nuclear magnetic resonance imaging (NMRI) is an objective and precise outcome measure for evaluating disease progression in neuromuscular disorders. We aimed to investigate predictive ‘disease activity’ NMR indices, including water T(2) and (31)P NMR spectroscopy (NMRS), and...

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Detalhes bibliográficos
Publicado no:Quant Imaging Med Surg
Principais autores: Reyngoudt, Harmen, Marty, Benjamin, Caldas de Almeida Araújo, Ericky, Baudin, Pierre-Yves, Le Louër, Julien, Boisserie, Jean-Marc, Béhin, Anthony, Servais, Laurent, Gidaro, Teresa, Carlier, Pierre G.
Formato: Artigo
Idioma:Inglês
Publicado em: AME Publishing Company 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7358411/
https://ncbi.nlm.nih.gov/pubmed/32676364
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.21037/qims-20-39
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