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Kidney Transplant in Fabry Disease: A Revision of the Literature

Fabry disease is classified as a rare X-linked disease caused by a complete or partial defect of enzyme alpha-galactosidase, due to GLA gene mutations. This disorder leads to intracellular globotriaosylceramide (Gb3) deposition associated with increased Gb3 plasma levels. Most of the symptoms of the...

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Detalhes bibliográficos
Publicado no:Medicina (Kaunas)
Main Authors: Capelli, Irene, Aiello, Valeria, Gasperoni, Lorenzo, Comai, Giorgia, Corradetti, Valeria, Ravaioli, Matteo, Biagini, Elena, Graziano, Claudio, La Manna, Gaetano
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7353860/
https://ncbi.nlm.nih.gov/pubmed/32532136
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/medicina56060284
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