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Astrocyte–microglial association and matrix composition are common events in the natural history of primary familial brain calcification

Primary familial brain calcification (PFBC) is an age‐dependent and rare neurodegenerative disorder characterized by microvascular calcium phosphate deposits in the deep brain regions. Known genetic causes of PFBC include loss‐of‐function mutations in genes involved in either of three processes—plat...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Brain Pathol
Egile Nagusiak: Nahar, Khayrun, Lebouvier, Thibaud, Andaloussi Mäe, Maarja, Konzer, Anne, Bergquist, Jonas, Zarb, Yvette, Johansson, Bengt, Betsholtz, Christer, Vanlandewijck, Michael
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: John Wiley and Sons Inc. 2019
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC7317599/
https://ncbi.nlm.nih.gov/pubmed/31561281
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/bpa.12787
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