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An Autopsy Case of Mixed Connective Tissue Disease Complicated by Thrombotic Thrombocytopenic Purpura

We herein report a patient with mixed connective tissue disease (MCTD) who had been stable for years but suddenly developed thrombotic thrombocytopenic purpura (TTP). The patient showed a clinical pentad of signs of TTP, low activity of ADAMTS13, and positivity of anti-ADAMTS13 antibodies. She did n...

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Dades bibliogràfiques
Publicat a:Intern Med
Autors principals: Furuya, Makiko Yashiro, Watanabe, Hiroshi, Sato, Shuzo, Fujita, Yuya, Tenmoku, Jumpei, Matsuoka, Naoki, Asano, Tomoyuki, Suzuki, Eiji, Kobayashi, Hiroko, Migita, Kiyoshi
Format: Artigo
Idioma:Inglês
Publicat: The Japanese Society of Internal Medicine 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7303452/
https://ncbi.nlm.nih.gov/pubmed/32418955
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.3939-19
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