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Emergency management in epidermolysis bullosa: consensus clinical recommendations from the European reference network for rare skin diseases

Epidermolysis bullosa (EB) comprises a group of genetic disorders with the hallmark of fragility of the skin and mucosal surfaces. The severity of different types of EB varies markedly as does the occurrence of extra-cutaneous involvement and complications. A number of emergency situations may occur...

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Dettagli Bibliografici
Pubblicato in:Orphanet J Rare Dis
Autori principali: Mellerio, Jemima E., El Hachem, Maya, Bellon, Nathalia, Zambruno, Giovanna, Buckova, Hana, Autrata, Rudolf, Salavastru, Carmen, Caldaro, Tamara, Greco, Celine, Has, Cristina, Bodemer, Christine
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7276067/
https://ncbi.nlm.nih.gov/pubmed/32505191
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-020-01403-x
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