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Alpha-1 Antitrypsin Deficiency and Pulmonary Morbidity in Patients with Primary Immunodeficiency Disease: A Single-Center Experience

BACKGROUND: Alpha-1 antitrypsin deficiency (AATD) is of importance in the pathogenesis of pulmonary emphysema, chronic obstructive pulmonary diseases (COPD), and bronchiectasis. Various pulmonary disorders are a typical feature of primary immunodeficiency disease (PID). This includes recurrent pulmo...

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Détails bibliographiques
Publié dans:Can Respir J
Auteurs principaux: Evers, Georg, Schulze, Arik Bernard, Thrull, Michael, Hering, Jan-Philipp, Schülke, Christoph, Wiewrodt, Rainer, Wittkowski, Helmut, Schmidt, Lars Henning, Mohr, Michael
Format: Artigo
Langue:Inglês
Publié: Hindawi 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7273390/
https://ncbi.nlm.nih.gov/pubmed/32566054
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2020/4019608
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