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Microphthalmia transcription factor expression contributes to bone marrow failure in Fanconi anemia

Hematopoietic stem cell (HSC) attrition is considered the key event underlying progressive BM failure (BMF) in Fanconi anemia (FA), the most frequent inherited BMF disorder in humans. However, despite major advances, how the cellular, biochemical, and molecular alterations reported in FA lead to HSC...

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Dettagli Bibliografici
Pubblicato in:J Clin Invest
Autori principali: Oppezzo, Alessia, Bourseguin, Julie, Renaud, Emilie, Pawlikowska, Patrycja, Rosselli, Filippo
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7269568/
https://ncbi.nlm.nih.gov/pubmed/31877112
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI131540
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