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Mitochondria dysfunction and metabolic reprogramming as drivers of idiopathic pulmonary fibrosis

Idiopathic pulmonary fibrosis (IPF) is a devastating lung disease of unknown etiology. It is characterized by deposition of extracellular matrix proteins, like collagen and fibronectin in the lung interstitium leading to respiratory failure. Our understanding of the pathobiology underlying IPF is st...

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Publicado en:Redox Biol
Main Authors: Bueno, Marta, Calyeca, Jazmin, Rojas, Mauricio, Mora, Ana L.
Formato: Artigo
Idioma:Inglês
Publicado: Elsevier 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7251240/
https://ncbi.nlm.nih.gov/pubmed/32234292
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.redox.2020.101509
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