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Novel MAG Variant Causes Cerebellar Ataxia with Oculomotor Apraxia: Molecular Basis and Expanded Clinical Phenotype

Homozygous variants in MAG, encoding myelin-associated glycoprotein (MAG), have been associated with complicated forms of hereditary spastic paraplegia (HSP). MAG is a glycoprotein member of the immunoglobulin superfamily, expressed by myelination cells. In this study, we identified a novel homozygo...

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Опубликовано в: :J Clin Med
Главные авторы: Santos, Mariana, Damásio, Joana, Kun-Rodrigues, Célia, Barbot, Clara, Sequeiros, Jorge, Brás, José, Alonso, Isabel, Guerreiro, Rita
Формат: Artigo
Язык:Inglês
Опубликовано: MDPI 2020
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC7230264/
https://ncbi.nlm.nih.gov/pubmed/32340215
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/jcm9041212
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