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Muscle Carnitine Palmitoyltransferase II (CPT II) Deficiency: A Conceptual Approach

Carnitine palmitoyltransferase (CPT) catalyzes the transfer of long- and medium-chain fatty acids from cytoplasm into mitochondria, where oxidation of fatty acids takes place. Deficiency of CPT enzyme is associated with rare diseases of fatty acid metabolism. CPT is present in two subforms: CPT I at...

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Bibliografske podrobnosti
izdano v:Molecules
Main Authors: Joshi, Pushpa Raj, Zierz, Stephan
Format: Artigo
Jezik:Inglês
Izdano: MDPI 2020
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC7221885/
https://ncbi.nlm.nih.gov/pubmed/32295037
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/molecules25081784
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