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Muscle Carnitine Palmitoyltransferase II (CPT II) Deficiency: A Conceptual Approach

Carnitine palmitoyltransferase (CPT) catalyzes the transfer of long- and medium-chain fatty acids from cytoplasm into mitochondria, where oxidation of fatty acids takes place. Deficiency of CPT enzyme is associated with rare diseases of fatty acid metabolism. CPT is present in two subforms: CPT I at...

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Detalhes bibliográficos
Publicado no:Molecules
Main Authors: Joshi, Pushpa Raj, Zierz, Stephan
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7221885/
https://ncbi.nlm.nih.gov/pubmed/32295037
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/molecules25081784
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