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SUN-366 Neonatal Severe Hyperparathyroidism: Extreme Hypercalcemia as a Robust Marker for Homozygous Dosage of Pathogenic CASR Variants

Context: Neonatal severe hyperparathyroidism (NSHPT) is a rare and life-threatening emergency. It includes generalized hyperparathyroid bone disease and respiratory distress from combinations among a narrowed thorax, rib fractures, hypotonia, and biochemical disturbances. Successful therapy is compa...

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Detalhes bibliográficos
Publicado no:J Endocr Soc
Main Authors: Marx, Stephen J, Sinaii, Ninet
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7207666/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jendso/bvaa046.024
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