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Simplified Diet for nutrition management of phenylketonuria: A survey of U.S. metabolic dietitians

BACKGROUND: Phenylketonuria (PKU) is an inherited metabolic disorder affecting the conversion of phenylalanine (Phe) to tyrosine. Medical nutrition therapy, consisting of a Phe‐restricted diet with medical formula, is the primary treatment for PKU. The Simplified Diet is an approach to PKU nutrition...

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Dettagli Bibliografici
Pubblicato in:JIMD Rep
Autori principali: Hansen, Joyanna, Hollander, Suzanne, Drilias, Nicoletta, Van Calcar, Sandra, Rohr, Fran, Bernstein, Laurie
Natura: Artigo
Lingua:Inglês
Pubblicazione: John Wiley & Sons, Inc. 2020
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7203646/
https://ncbi.nlm.nih.gov/pubmed/32395413
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jmd2.12106
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