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Diagnostic Value of Anthropometric Measurements for Familial Partial Lipodystrophy, Dunnigan Variety

CONTEXT: Familial partial lipodystrophy, Dunnigan variety (FPLD2) is a rare autosomal dominant disorder resulting from LMNA causal variants, which is characterized by loss of subcutaneous fat from the extremities and predisposition to metabolic complications. The diagnostic value of various anthropo...

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Détails bibliographiques
Publié dans:J Clin Endocrinol Metab
Auteurs principaux: Vasandani, Chandna, Li, Xilong, Sekizkardes, Hilal, Adams-Huet, Beverley, Brown, Rebecca J, Garg, Abhimanyu
Format: Artigo
Langue:Inglês
Publié: Oxford University Press 2020
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Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7202860/
https://ncbi.nlm.nih.gov/pubmed/32193531
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/clinem/dgaa137
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