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Management of Pulmonary Arterial Hypertension in Patients with Systemic Sclerosis

Systemic sclerosis (SSc) is a rare and complex immune-mediated connective tissue disease characterized by multi-organ fibrosis and dysfunction. Systemic sclerosis-associated pulmonary arterial hypertension (SSc-PAH) is a leading cause of death in this population. Pulmonary arterial hypertension (PAH...

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Detalhes bibliográficos
Publicado no:Integr Blood Press Control
Main Authors: Almaaitah, Saja, Highland, Kristin B, Tonelli, Adriano R
Formato: Artigo
Idioma:Inglês
Publicado em: Dove 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7125406/
https://ncbi.nlm.nih.gov/pubmed/32280271
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/IBPC.S232038
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