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Hereditary Diffuse Gastric Cancer: Updated Clinical Practice Guidelines

Hereditary Diffuse Gastric Cancer (HDGC) is an autosomal dominant cancer syndrome that is characterised by a high prevalence of diffuse gastric cancer and lobular breast cancer. It is largely caused by inactivating germline mutations in the tumour suppressor gene CDH1, although pathogenic variants i...

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Publié dans:Lancet Oncol
Auteurs principaux: Blair, Vanessa R, McLeod, Maybelle, Carneiro, Fátima, Coit, Daniel G, D’Addario, Johanna L, van Dieren, Jolanda M, Harris, Kirsty L, Hoogerbrugge, Nicoline, Oliveira, Carla, van der Post, Rachel S, Arnold, Julie, Benusiglio, Patrick R, Bisseling, Tanya M, Boussioutas, Alex, Cats, Annemieke, Charlton, Amanda, Chelcun Schreiber, Karen E, Davis, Jeremy L, di Pietro, Massimiliano, Fitzgerald, Rebecca, Ford, James M, Gamet, Kimberley, Gullo, Irene, Hardwick, Richard H, Huntsman, David G, Kaurah, Pardeep, Kupfer, Sonia S, Latchford, Andrew, Mansfield, Paul F, Nakajima, Takeshi, Parry, Susan, Rossaak, Jeremy, Sugimura, Haruhiko, Svrcek, Magali, Tischkowitz, Marc, Ushijima, Toshikazu, Yamada, Hidetaka, Yang, Han-Kwang, Claydon, Adrian, Figueiredo, Joana, Paringatai, Karyn, Seruca, Raquel, Bougen-Zhukov, Nicola, Brew, Tom, Busija, Simone, Carneiro, Patricia, DeGregorio, Lynn, Fisher, Helen, Gardner, Erin, Godwin, Tanis D, Holm, Katharine N, Humar, Bostjan, Lintott, Caroline J, Monroe, Elizabeth C, Muller, Mark D, Norero, Enrique, Nouri, Yasmin, Paredes, Joana, Sanches, João, Schulpen, Emily, Ribeiro, Ana Sofia, Sporle, Andrew, Whitworth, James, Zhang, Liying, Reeve, Anthony E, Guilford, Parry
Format: Artigo
Langue:Inglês
Publié: 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7116190/
https://ncbi.nlm.nih.gov/pubmed/32758476
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/S1470-2045(20)30219-9
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