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Comparative proteomic analyses of Duchenne muscular dystrophy and Becker muscular dystrophy muscles: changes contributing to preserve muscle function in Becker muscular dystrophy patients

BACKGROUND: Duchenne muscular dystrophy (DMD) and Becker muscular dystrophy (BMD) are characterized by muscle wasting leading to loss of ambulation in the first or third decade, respectively. In DMD, the lack of dystrophin hampers connections between intracellular cytoskeleton and cell membrane lead...

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Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:J Cachexia Sarcopenia Muscle
Egile Nagusiak: Capitanio, Daniele, Moriggi, Manuela, Torretta, Enrica, Barbacini, Pietro, De Palma, Sara, Viganò, Agnese, Lochmüller, Hanns, Muntoni, Francesco, Ferlini, Alessandra, Mora, Marina, Gelfi, Cecilia
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: John Wiley and Sons Inc. 2020
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC7113522/
https://ncbi.nlm.nih.gov/pubmed/31991054
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jcsm.12527
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