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Rescuing compounds for Lesch-Nyhan disease identified using stem cell–based phenotypic screening

Lesch-Nyhan disease (LND) is a rare monogenic disease caused by deficiency of the salvage pathway enzyme hypoxanthine-guanine phosphoribosyltransferase (HGPRT). LND is characterized by severe neuropsychiatric symptoms that currently cannot be treated. Predictive in vivo models are lacking for screen...

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Détails bibliographiques
Publié dans:JCI Insight
Auteurs principaux: Ruillier, Valentin, Tournois, Johana, Boissart, Claire, Lasbareilles, Marie, Mahé, Gurvan, Chatrousse, Laure, Cailleret, Michel, Peschanski, Marc, Benchoua, Alexandra
Format: Artigo
Langue:Inglês
Publié: American Society for Clinical Investigation 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7101145/
https://ncbi.nlm.nih.gov/pubmed/31990683
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.132094
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