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Fatigability in spinal muscular atrophy: validity and reliability of endurance shuttle tests

BACKGROUND: To determine construct validity and test-retest reliability of Endurance Shuttle Tests as outcome measures for fatigability of remaining motor functions in children and adults with Spinal Muscular Atrophy (SMA) across the severity spectrum. RESULTS: We assessed the Endurance Shuttle - Ni...

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Dettagli Bibliografici
Pubblicato in:Orphanet J Rare Dis
Autori principali: Bartels, Bart, de Groot, Janke F., Habets, Laura E., Wijngaarde, Camiel A., Vink, Wendy, Stam, Marloes, Asselman, Fay-Lynn, van Eijk, Ruben P. A., van der Pol, W. Ludo
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7092552/
https://ncbi.nlm.nih.gov/pubmed/32293503
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-020-1348-2
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