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Alpha 1-Antitrypsin Deficiency: A Disorder of Proteostasis-Mediated Protein Folding and Trafficking Pathways

Human cells express large amounts of different proteins continuously that must fold into well-defined structures that need to remain correctly folded and assemble in order to ensure their cellular and biological functions. The integrity of this protein balance/homeostasis, also named proteostasis, i...

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Publicat a:Int J Mol Sci
Autors principals: Karatas, Esra, Bouchecareilh, Marion
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7073043/
https://ncbi.nlm.nih.gov/pubmed/32098273
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21041493
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