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Impact on Isoleucine and Valine Supplementation When Decreasing Use of Medical Food in the Nutritional Management of Methylmalonic Acidemia

Background: Methylmalonic acidemia (MMA) is an autosomal recessive disorder treated with precursor-free medical food while limiting natural protein. This retrospective chart review was to determine if there was a relationship between medical food, valine (VAL) and/or isoleucine (ILE) supplementation...

Täydet tiedot

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Bibliografiset tiedot
Julkaisussa:Nutrients
Päätekijät: Bernstein, Laurie E., Burns, Casey, Drumm, Morgan, Gaughan, Sommer, Sailer, Melissa, Baker II, Peter R.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: MDPI 2020
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7071216/
https://ncbi.nlm.nih.gov/pubmed/32069872
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu12020473
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