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An update on the genetics and pathogenesis of hereditary angioedema

Hereditary angioedema (HAE) is an uncommon genetic disorder characterized by recurrent episodes of edema involving subcutaneous tissue and submucosa. The pathogenesis of HAE reflects an intricate coordinated regulation of components of complement, kinin and hemostatic pathway. Till date, mutations i...

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Kaydedildi:
Detaylı Bibliyografya
Yayımlandı:Genes Dis
Asıl Yazarlar: Banday, Aaqib Zaffar, Kaur, Anit, Jindal, Ankur Kumar, Rawat, Amit, Singh, Surjit
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Chongqing Medical University 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC7063419/
https://ncbi.nlm.nih.gov/pubmed/32181278
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.gendis.2019.07.002
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