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Familial “benign” pemphigus? Erythroderma and fatal outcome()()

Hailey–Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual cas...

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Bibliographic Details
Published in:An Bras Dermatol
Main Authors: Tansini, Paula Baldissera, Boff, Ana Letícia, Weber, Magda Blessmann, Bonamigo, Renan Rangel
Format: Artigo
Language:Inglês
Published: Sociedade Brasileira de Dermatologia 2020
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Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC7058835/
https://ncbi.nlm.nih.gov/pubmed/31959512
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.abd.2019.02.006
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