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Globoid Cell Leukodystrophy: Distinguishing Early-Onset from Late-Onset Disease Using a Brain MR Imaging Scoring Method

BACKGROUND AND PURPOSE: Our purpose was to determine the characteristic MR features of early-onset (before age 2 years) versus late-onset (after age 2 years) globoid cell leukodystrophy (GLD). METHODS: Thirty-four brain MR images in 22 patients with GLD were reviewed. A severity score (0 to 32), bas...

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Publicat a:AJNR Am J Neuroradiol
Autors principals: Loes, Daniel J., Peters, Charles, Krivit, William
Format: Artigo
Idioma:Inglês
Publicat: American Society of Neuroradiology 1999
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7056124/
https://ncbi.nlm.nih.gov/pubmed/10094363
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