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Ratio of Fabry disease in patients with idiopathic left ventricular hypertrophy: A single-center study in Turkey

OBJECTIVE: Fabry disease (FD) is a progressive, X-linked inherited disorder of glycosphingolipid metabolism which arises due to deficient or absent activity of lysosomal α-galactosidase A (α-Gal A). This may be associated with increased left ventricular (LV) wall thickness and may mimic the morpholo...

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Detalhes bibliográficos
Publicado no:Anatol J Cardiol
Main Authors: Barman, Hasan Ali, Özcan, Sevgi, Atıcı, Adem, Özgökçe, Caner, Öztürk, Ahmet, Kafalı, Ayşegül Ezgi, Çakar, Nafiye Emel, Tavşanlı, Mustafa Emir, Küçük, Mehmet, Şahin, İrfan, Okuyan, Ertuğrul
Formato: Artigo
Idioma:Inglês
Publicado em: Kare Publishing 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7040871/
https://ncbi.nlm.nih.gov/pubmed/32011328
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.14744/AnatolJCardiol.2019.84782
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