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Pirfenidone in idiopathic pulmonary fibrosis: real-life experience in the referral centre of Siena

BACKGROUND: Idiopathic pulmonary fibrosis (IPF) is the most common idiopathic interstitial pneumonia and has a median survival after diagnosis of 2–5 years. Pirfenidone is the first approved antifibrotic drug for the treatment of IPF. Here we report the functional progress, side effects and survival...

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Pubblicato in:Ther Adv Respir Dis
Autori principali: Vietri, Lucia, Cameli, Paolo, Perruzza, Marco, Cekorja, Behar, Bergantini, Laura, d’Alessandro, Miriana, Refini, Rosa Metella, Pieroni, Maria, Fossi, Antonella, Bennett, David, Spalletti, Marco, Mazzei, Maria Antonietta, Sestini, Piersante, Rottoli, Paola, Bargagli, Elena
Natura: Artigo
Lingua:Inglês
Pubblicazione: SAGE Publications 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7029533/
https://ncbi.nlm.nih.gov/pubmed/32066332
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1753466620906326
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