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Chronic intestinal pseudo-obstruction due to β2microglobulin-amyloidosis in a patient on high-flux haemodialysis

Dialysis-related amyloidosis (DRA) or β2microglobulin (β2m)-amyloidosis is a disorder caused by the inability to clear a protein called β2m in patients with chronic kidney disease. It results in deposition of β2m as amyloid fibrils, most commonly in bones and joints. Infrequently, visceral organs ma...

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Dades bibliogràfiques
Publicat a:BMJ Case Rep
Autors principals: De Mulder, Pieter, Cokelaere, Kristof, Terryn, Wim
Format: Artigo
Idioma:Inglês
Publicat: BMJ Publishing Group 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7021141/
https://ncbi.nlm.nih.gov/pubmed/31980473
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2019-232201
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