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A Krüppel-like factor 1 (KLF1) Mutation Associated with Severe Congenital Dyserythropoietic Anemia Alters Its DNA-Binding Specificity

Krüppel-like factor 1 (KLF1/EKLF) is a transcription factor that globally activates genes involved in erythroid cell development. Various mutations are identified in the human KLF1 gene. The E325K mutation causes congenital dyserythropoietic anemia (CDA) type IV, characterized by severe anemia and n...

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Pubblicato in:Mol Cell Biol
Autori principali: Kulczynska, Klaudia, Bieker, James J., Siatecka, Miroslawa
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Microbiology 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7020642/
https://ncbi.nlm.nih.gov/pubmed/31818881
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1128/MCB.00444-19
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