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Idiopathic Pulmonary Fibrosis: Best Practice in Monitoring and Managing a Relentless Fibrotic Disease

Idiopathic pulmonary fibrosis (IPF) is a fibrosing interstitial lung disease that is, by definition, progressive. Progression of IPF is reflected by a decline in lung function, worsening of dyspnea and exercise capacity, and deterioration in health-related quality of life. In the short term, the cou...

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Publicado en:Respiration
Autores principales: Wuyts, Wim A., Wijsenbeek, Marlies, Bondue, Benjamin, Bouros, Demosthenes, Bresser, Paul, Robalo Cordeiro, Carlos, Hilberg, Ole, Magnusson, Jesper, Manali, Effrosyni D., Morais, António, Papiris, Spyridon, Shaker, Saher, Veltkamp, Marcel, Bendstrup, Elisabeth
Formato: Artigo
Lenguaje:Inglês
Publicado: S. Karger AG 2020
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6979429/
https://ncbi.nlm.nih.gov/pubmed/31830755
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000504763
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