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FMF is not always “fever”: from clinical presentation to “treat to target”

Familial Mediterranean Fever, a monogenic autoinflammatory disease secondary to MEFV gene mutations in the chromosome 16p13, is characterized by recurrent self-limiting attacks of fever, arthritis, aphthous changes in lips and/or oral mucosa, erythema, serositis. It is caused by dysregulation of the...

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Detalles Bibliográficos
Publicado en:Ital J Pediatr
Main Authors: Maggio, Maria Cristina, Corsello, Giovanni
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2020
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6961393/
https://ncbi.nlm.nih.gov/pubmed/31941537
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13052-019-0766-z
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