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Severe but reversible pulmonary hypertension in scleromyxedema and multiple myeloma: a case report

BACKGROUND: Scleromyxedema is a progressive, systemic connective tissue disorder characterized by fibro-mucous skin lesions and increased serum monoclonal immunoglobulin levels. Pulmonary involvement occurs in a subset of patients, though the overall prevalence of pulmonary lesions in scleromyxedema...

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Publicado en:BMC Pulm Med
Autores principales: Kreidy, Mazen, Al-Hilli, Ali, Yachoui, Ralph, Resnick, Jeffrey
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2020
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6953266/
https://ncbi.nlm.nih.gov/pubmed/31918690
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12890-019-1020-6
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