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Amyotrophic lateral sclerosis associated with pleuroparenchymal fibroelastosis

An autopsy case of sporadic amyotrophic lateral sclerosis (ALS) associated with pleuroparenchymal fibroelastosis (PPFE), a rare form of idiopathic interstitial pneumonia, is reported. The patient, a 76-year-old man, presented with shortness of breath and dyspnea and died of progressive respiratory f...

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Pubblicato in:Int J Clin Exp Pathol
Autori principali: Shintaku, Masayuki, Takeuchi, Hitoshi, Ando, Koichi, Kobayashi, Yugo, Hasegawa, Hiroshi
Natura: Artigo
Lingua:Inglês
Pubblicazione: e-Century Publishing Corporation 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6949758/
https://ncbi.nlm.nih.gov/pubmed/31933790
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