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Primary Immunodeficiency with Severe Multi-Organ Immune Dysregulation

Polyglandular autoimmune syndrome type 1, also known as autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED), is a rare primary immunodeficiency disorder with multi-organ involvement. Besides for being predisposed to severe life-threatening infections, patients with APECED are als...

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Dades bibliogràfiques
Publicat a:Case Reports Immunol
Autor principal: Gavrilova, Tatyana
Format: Artigo
Idioma:Inglês
Publicat: Hindawi 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6949663/
https://ncbi.nlm.nih.gov/pubmed/31956453
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2019/8746249
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