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Natural and pathogenic protein sequence variation affecting prion-like domains within and across human proteomes

BACKGROUND: Impaired proteostatic regulation of proteins with prion-like domains (PrLDs) is associated with a variety of human diseases including neurodegenerative disorders, myopathies, and certain forms of cancer. For many of these disorders, current models suggest a prion-like molecular mechanism...

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Publicat a:BMC Genomics
Autors principals: Cascarina, Sean M., Ross, Eric D.
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6947906/
https://ncbi.nlm.nih.gov/pubmed/31914925
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12864-019-6425-3
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