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Metabolic Alterations in Cardiomyocytes of Patients with Duchenne and Becker Muscular Dystrophies

Duchenne and Becker muscular dystrophies (DMD/BMD) result in progressive weakness of skeletal and cardiac muscles due to the deficiency of functional dystrophin. Respiratory failure is a leading cause of mortality in DMD patients; however, improved management of the respiratory symptoms have increas...

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Pubblicato in:J Clin Med
Autori principali: Esposito, Gabriella, Carsana, Antonella
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6947625/
https://ncbi.nlm.nih.gov/pubmed/31817415
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/jcm8122151
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