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Defects in Axonal Transport in Inherited Neuropathies

Axonal transport is a highly complex process essential for sustaining proper neuronal functioning. Disturbances can result in an altered neuronal homeostasis, aggregation of cargoes, and ultimately a dying-back degeneration of neurons. The impact of dysfunction in axonal transport is shown by geneti...

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Dettagli Bibliografici
Pubblicato in:J Neuromuscul Dis
Autori principali: Beijer, Danique, Sisto, Angela, Van Lent, Jonas, Baets, Jonathan, Timmerman, Vincent
Natura: Artigo
Lingua:Inglês
Pubblicazione: IOS Press 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6918914/
https://ncbi.nlm.nih.gov/pubmed/31561383
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JND-190427
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