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Dynamic respiratory muscle function in late-onset Pompe disease

Maximal inspiratory pressure (PI(MAX)) reflects inspiratory weakness in late-onset Pompe disease (LOPD). However, static pressure tests may not reveal specific respiratory muscle adaptations to disruptions in breathing. We hypothesized that dynamic respiratory muscle functional tests reflect distinc...

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Publicat a:Sci Rep
Autors principals: Smith, Barbara K., Allen, Shannon, Mays, Samantha, Martin, A. Daniel, Byrne, Barry J.
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group UK 2019
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6908708/
https://ncbi.nlm.nih.gov/pubmed/31831753
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-019-54314-8
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