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Dynamic respiratory muscle function in late-onset Pompe disease
Maximal inspiratory pressure (PI(MAX)) reflects inspiratory weakness in late-onset Pompe disease (LOPD). However, static pressure tests may not reveal specific respiratory muscle adaptations to disruptions in breathing. We hypothesized that dynamic respiratory muscle functional tests reflect distinc...
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| Publicat a: | Sci Rep |
|---|---|
| Autors principals: | , , , , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Nature Publishing Group UK
2019
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6908708/ https://ncbi.nlm.nih.gov/pubmed/31831753 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-019-54314-8 |
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