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Tracking muscle wasting and disease activity in facioscapulohumeral muscular dystrophy by qualitative longitudinal imaging

BACKGROUND: Facioscapulohumeral muscular dystrophy (FSHD) is one of the most frequent late‐onset muscular dystrophies, characterized by progressive fatty replacement and degeneration involving single muscles in an asynchronous manner. With clinical trials at the horizon in this disease, the knowledg...

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Publicat a:J Cachexia Sarcopenia Muscle
Autors principals: Monforte, Mauro, Laschena, Francesco, Ottaviani, Pierfrancesco, Bagnato, Maria Rosaria, Pichiecchio, Anna, Tasca, Giorgio, Ricci, Enzo
Format: Artigo
Idioma:Inglês
Publicat: John Wiley and Sons Inc. 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6903444/
https://ncbi.nlm.nih.gov/pubmed/31668022
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jcsm.12473
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