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Serum complexes between C1INH and C1INH autoantibodies for the diagnosis of acquired angioedema

Acquired angioedema due to C1‐inhibitor (C1INH) deficiency (AAE) is caused by secondary C1INH deficiency leading to bradykinin‐mediated angioedema episodes. AAE typically presents in adulthood and is associated with B cell lymphoproliferation. Anti‐C1INH autoantibodies (antiC1INHAbs) are detectable...

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Detalles Bibliográficos
Publicado en:Clin Exp Immunol
Main Authors: López‐Lera, A., Garrido, S., Nozal, P., Skatum, L., Bygum, A., Caballero, T., López Trascasa, M.
Formato: Artigo
Idioma:Inglês
Publicado: John Wiley and Sons Inc. 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6857074/
https://ncbi.nlm.nih.gov/pubmed/31397881
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/cei.13361
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