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Low fat diets increase survival of a mouse model of spinal muscular atrophy

Spinal muscular atrophy (SMA) is a neuromuscular disorder leading to paralysis and death. Recent evidence shows increased susceptibility to dyslipidemia and liver steatosis in patients. Here, we provide evidence that low fat diets nearly double survival in Smn(2B/−) mice, a model for SMA, independen...

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Detalhes bibliográficos
Publicado no:Ann Clin Transl Neurol
Main Authors: Deguise, Marc‐Olivier, Chehade, Lucia, Tierney, Alexandra, Beauvais, Ariane, Kothary, Rashmi
Formato: Artigo
Idioma:Inglês
Publicado em: John Wiley and Sons Inc. 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6856606/
https://ncbi.nlm.nih.gov/pubmed/31608604
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/acn3.50920
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