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Low increase in phenylalanine tolerance during pregnancies in PKU woman with high prepregnancy BMI and postconceptional initiation of diet: A case report

BACKGROUND: Women with untreated phenylketonuria (PKU) are at an increased risk to have offspring with multiple abnormalities due to teratogenic effects of hyperphenylalaninaemia. Treatment goals include blood phenylalanine concentrations between 120 and 360 µmol/L, however, there are limited pieces...

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Detaylı Bibliyografya
Yayımlandı:Int J Reprod Biomed (Yazd)
Asıl Yazarlar: Żółkowska, Joanna, Hozyasz, Kamil, Ph.D.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Knowledge E 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6844282/
https://ncbi.nlm.nih.gov/pubmed/31807725
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.18502/ijrm.v17i10.5302
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