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Evidence of Cardiovascular Calcification and Fibrosis in Pseudoxanthoma Elasticum Mouse Models Subjected to DOCA-Salt Hypertension

Pseudoxanthoma Elasticum (PXE) is a rare disorder characterized by fragmentation and progressive calcification of elastic fibres in connective tissues. Although arterial hypertension (AHT) has been reported in PXE patients, its impact on pathological manifestations has as yet been unexplored. We inv...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Omarjee, Loukman, Roy, Charlotte, Leboeuf, Christophe, Favre, Julie, Henrion, Daniel, Mahe, Guillaume, Leftheriotis, Georges, Martin, Ludovic, Janin, Anne, Kauffenstein, Gilles
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group UK 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6841718/
https://ncbi.nlm.nih.gov/pubmed/31704980
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-019-52808-z
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