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Evidence of Cardiovascular Calcification and Fibrosis in Pseudoxanthoma Elasticum Mouse Models Subjected to DOCA-Salt Hypertension

Pseudoxanthoma Elasticum (PXE) is a rare disorder characterized by fragmentation and progressive calcification of elastic fibres in connective tissues. Although arterial hypertension (AHT) has been reported in PXE patients, its impact on pathological manifestations has as yet been unexplored. We inv...

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Detalhes bibliográficos
Publicado no:Sci Rep
Main Authors: Omarjee, Loukman, Roy, Charlotte, Leboeuf, Christophe, Favre, Julie, Henrion, Daniel, Mahe, Guillaume, Leftheriotis, Georges, Martin, Ludovic, Janin, Anne, Kauffenstein, Gilles
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group UK 2019
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6841718/
https://ncbi.nlm.nih.gov/pubmed/31704980
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-019-52808-z
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