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Daily Fructose Traces Intake and Liver Injury in Children with Hereditary Fructose Intolerance

Background: Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury bioma...

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Publicado en:Nutrients
Main Authors: Di Dato, Fabiola, Spadarella, Simona, Puoti, Maria Giovanna, Caprio, Maria Grazia, Pagliardini, Severo, Zuppaldi, Claudia, Vallone, Gianfranco, Fecarotta, Simona, Esposito, Gabriella, Iorio, Raffaele, Parenti, Giancarlo, Spagnuolo, Maria Immacolata
Formato: Artigo
Idioma:Inglês
Publicado: MDPI 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6835214/
https://ncbi.nlm.nih.gov/pubmed/31591370
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu11102397
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