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2287 ECG and echo characteristics in familial partial lipodystrophy: The impact of Lamin A variants

OBJECTIVES/SPECIFIC AIMS: Familial partial lipodystrophy (FPLD) is an inherited, rare syndrome characterized by selective absence of adipose tissue from extremities which is associated with severe insulin resistance, and metabolic dyslipidemia (with hypertriglyceridemia, and low HDL) Typically, 30%–...

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Pubblicato in:J Clin Transl Sci
Autori principali: Eldin, Abdelwahab J., Meral, Rasimcan, Neidert, Adam H., Rus, Diana, Hench, Rita, Oral, Hakan, Oral, Elif A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Cambridge University Press 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6798885/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1017/cts.2018.164
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