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Expression and Endocytosis of Lysosomal Aspartylglucosaminidase in Mouse Primary Neurons

Aspartylglucosaminuria (AGU) is a neurodegenerative lysosomal storage disease that is caused by mutations in the gene encoding for a soluble hydrolase, aspartylglucosaminidase (AGA). In this study, we have used our recently developed mouse model for AGU and analyzed processing, intracellular localiz...

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Détails bibliographiques
Publié dans:J Neurosci
Auteurs principaux: Kyttälä, Aija, Heinonen, Outi, Peltonen, Leena, Jalanko, Anu
Format: Artigo
Langue:Inglês
Publié: Society for Neuroscience 1998
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC6793022/
https://ncbi.nlm.nih.gov/pubmed/9742145
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.18-19-07750.1998
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