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Variably protease‐sensitive prionopathy mimicking frontotemporal dementia

Sporadic prion diseases are fatal neurodegenerative disorders characterized clinically by rapidly progressive dementia and myoclonus. Variably protease‐sensitive prionopathy (VPSPr) is a recently identified sporadic human prion disorder that may present with a lengthy atypical clinical history. Here...

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Detalhes bibliográficos
Publicado no:Neuropathology
Main Authors: Aizpurua, Miren, Selvackadunco, Sashika, Yull, Helen, Kipps, Christopher M., Ironside, James W., Bodi, Istvan
Formato: Artigo
Idioma:Inglês
Publicado em: John Wiley & Sons Australia, Ltd 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6778052/
https://ncbi.nlm.nih.gov/pubmed/30847986
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/neup.12538
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