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Retinal Phenotype in the rd9 Mutant Mouse, a Model of X-Linked RP

Retinal degeneration 9 (rd9) mice carry a mutation in the retina specific “Retinitis Pigmentosa GTPase Regulator (RPGR)” Open Reading Frame (ORF) 15 gene, located on the X chromosome and represent a rare model of X-linked Retinitis Pigmentosa (XLRP), a common and severe form of retinal degeneration...

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Dades bibliogràfiques
Publicat a:Front Neurosci
Autors principals: Falasconi, Antonio, Biagioni, Martina, Novelli, Elena, Piano, Ilaria, Gargini, Claudia, Strettoi, Enrica
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6761883/
https://ncbi.nlm.nih.gov/pubmed/31607844
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnins.2019.00991
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