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Basement membrane collagens and disease mechanisms

Basement membranes (BMs) are specialised extracellular matrix (ECM) structures and collagens are a key component required for BM function. While collagen IV is the major BM collagen, collagens VI, VII, XV, XVII and XVIII are also present. Mutations in these collagens cause rare multi-systemic diseas...

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Publicado en:Essays Biochem
Main Authors: Gatseva, Anna, Sin, Yuan Yan, Brezzo, Gaia, Van Agtmael, Tom
Formato: Artigo
Idioma:Inglês
Publicado: Portland Press Ltd. 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6744580/
https://ncbi.nlm.nih.gov/pubmed/31387942
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1042/EBC20180071
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